[01] Guru Dutta Satyarthee, Department of Neurosurgery, All India Institute of Medical Sciences, JPNA Trauma Centre, New Delhi, India. [02] Shikha Satyarthee, Department of Neurosurgery, All India Institute of Medical Sciences, JPNA Trauma Centre, New Delhi, India.

Background: Congenital occipital dermal sinus with an underlying dermoid is a rare, benign lesion of embryological origin and may occur anywhere along the neuraxis. Material and methods: A case of occipital region dermal sinus associated with cerebellar abscess is described. Result: A-10- year-old girl was admitted with complaints of fever, headache and vomiting, Neurological examination revealed stiff neck with papilloedema involving both eyes. She had ataxic gaits with cerebellar signs. The computerised tomography revealed multiple cerebellar abscesses. In emergency, she underwent midline suboccipital craniectomy; with excision of abscess and developed aseptic meningitis in the postoperative period, which responded to antimicrobial therapy. Conclusion: A case suspected with meningitis should all be looked for presence of sinus along the spinal and cranial axis, which may give clue to presence of the underlying dermoid cyst and abscess. The treating physician should aware of such although rare clinical entity as timely surgical intervention can yield good neurological outcome.

Epidermoid Cyst, Occipital Dermal Sinus, Cerebellar Abscess

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